He aha te mate Ollier. a Ollier mate: tātaritanga me te maimoatanga

e whakaaro koe e āta tupu koutou waewae tamaiti iti ringa ranei? Pea ia mate Ollier. Ko te mate i roto i nei i reira he abnormalities o te whanaketanga wheua o te kōhiwi, e ko, tona dysplasia. Ētahi atu ingoa whakahuatia mate - wheua chondromatosis maha, unilateral ranei chondromatosis diskhondroplaziya wheua. Ko tona mate taitara matua mo o taote Lyon Olier. Ko te mate kitea ia, ka whakaahuatia i roto i te whakamahi o te X-hihi i roto i te 1899.

He aha te mea te mate Ollier

E pā ana tēnei mate ki abnormalities o te kōhiwi a Ihakara, e no ki maha nga mate, tae atu ki te pai-mohiotia ki maha mama tamariki dysplasia hip.

te tikanga faaite te mate i roto i te tamarikitanga, no te mea o te mea i whakaaro i mua e tenei mate o tamariki. Kei te whakamatauria reira inaianei e taea e te māuiuitanga hanga tona tuatahi i roto i ngā pakeke (kia puta tohu ara i roto i te whānuitanga tau 20-40 tau). Ko te pīari congenital, engari kitea e ia i etahi wa i muri mai - i roto i te kōhungahunga ranei i roto i te taiohi - e ko, i te wa o te tupu kaha, ka riro te reira deformation kitea o wheua whanaketanga rerekē o nga ringa me nga waewae, me te / ranei.

mate a Ollier i te metaphyses o roa wheua tubular o rara, puta growths o ngohe. whakawhanake mate i te nuinga i roto i te wheua, ngohe, me hononga o nga ringa, me waewae, ngā i roto i te waewae, me ringa, me te i roto i te papatoiake, engari kua kitea te reira i roto i te rara, whaturei me te Angaanga.

Growths enhondromy ranei hanga te kahu waho o te wheua kikokore, me te he pakarukaru. I roto i te meka, he mea he puku Koló e taea te whakawhanake ki mārere (hei tauira, chondrosarcoma). Aua'e, tupu rawa uaua tenei.

I roto i te pūhuruhurutanga o ū me whakakapi e te wheua growths.

Ko te kupu, mate Ollier - taimaha mate tuku, calcification o te kōhiwi cartilaginous i roto i nei hoki puta me metaphyses thickening (wheua roa o te kaki). Ko te take hoki tona takanga ko tonu unknown. I roto i ētahi wā, he mea he huru ira tino autosomal.

Rite ki te diskhondroplaziey mate he syndromes onge maffucci me Proteus. I te tuatahi, motu ke i Koló growths wheua ngohe me deformities kōhiwi, kiri hemangioma i hanga - pouri wahi whero āhua kōhikohiko, arā, o oko toto. I roto i te puku Koló tuarua whakawhanake i roto i ngā wāhanga ngā o te tinana.

Ko wai pāngia e te mate

Mua i whakaaro ai e chondromatosis onge nga wheua. Tena ko tenei, ka kawea te whakamātautau X-ray e i roto i te whānui nui, ka tahuri te reira i roto i taua e kore ko reira te varavara. Ki te 20 matahiti i ma'iri a'e, i whakaahuatia ai 30 take e he rua ratou i teie nei rite tokomaha.

Hei whakatau i te tīmatanga tangohia te tikanga e taea ki te kore kua he whanau he ako hihiri auau te whakamahi i X-hihi, ina koa i roto i te kōhungahunga me te whanaketanga fetal, ka, i roto i te meka, mate Ollier reira. Ko te mate, ko te, i te ara, whakakitea te kotiro tata e rua nga wa atu pinepine atu i te mau tamaroa.

tohu

E kore e ki te mahue te tohu o te mate, kia kia tūpato ki te he tamaiti mau metua:

• roa i roto i te whanaketanga o ētahi wāhanga o te wahi / topito;
• karawhiti tohua me te shortening i roto ia ratou;
• totitoti, ua faariro;
• reira he misalignment o te papatoiake;
• curvature reira o nga hononga o valgus momo varus ranei.

enei āhuatanga katoa kia taea ki te amo i taua te mate Ollier tamaiti.

E kore te mea te mate tonu tonu kitea i whanau, engari i te tau o 1-4 tau, ka kite koutou e he pōturi ake i tūmanakohia te tamaiti, te whakanui ake i te waewae ringa ranei. Ko te tohu matua o te mate, e kore e taea te waiho tenei. Kei te whakawhanake te tikanga te toenga o te tamaiti, ahakoa te meka i pāngia ia ki "mate a Ollier."

tino maha Diskhondroplaziya pā kotahi e alangá, Heoi i reira he take o te mate e rua. Ki te mea kua pa te mate ki raro, te tamaiti ka hei tipu raro e tika ana ki to ratou shortening. Rawa kaha akaaka wheua, ki te tīmata wawe rawa te tukanga pathological. puta deformation mauiui puhoi ahunga whakamua. O te akoranga, te rongo ki te mate, riro poto, nui, te huri kiwi e, kitea totitoti, te. He pea he varus ranei valgus hira o te turi (iti maha - te pito rarahi o te pūkaka waewae ranei), scoliosis o te tuaiwi. e kore he reira uaua atrophy i roto i tenei mate.

He huringa Big raro ki te phalanx, metatarsal me, i roto i ētahi wā, te metacarpals. poroa, atu, hauwarea, me te wheua ngohe i roto i ratou maha enlightenments.

mate o Ollier pea ki te matiti rite ki te hua o te mate ratou whakawhanakehia te wheua he. Heoi, piere maha tura'i tupuria.

Comorbidities

Ka taea e Diskhondroplaziyu tahi pāpaka o te tahi atu whēkau, e kore e tonu ahakoa whakawhanake mate e pā ana. I roto i ngā, i roto i te mau tamahine taitamariki ki te mate o Ollier kia puta teratoma o te kura kākano me endocrine disorders, tae atu kino, tae atu paheke wawe rawa me pūhuruhurutanga precocious whakatere ossification.

Heoi, ka hoki te whanaketanga e ki noa mā te tango i te puku kura kākano.

tātaringa

Ki te tāutu i te mate o Ollier, he mea e tika ana te tuatahi ki te hanga i te Roentgen. He kia hoki kia he unuhanga wheua, me te atahanga te kōwarotanga autō. Ki runga ki te rapunga o te mate, e rapu tūroro auau Taki-ups i te tākuta, ki te tika, ki te tautuhi i hohoro te huringa mārere ki te chondrosarcoma.

tātaritanga pārōnaki

tātaritanga pārōnaki o te mate o Ollier, i roto i te meka, e kore e tika i muri i te X-ray, no te mea ko te pikitia chondromatosis rawa motuhake. Heoi, ko ia take takitahi, engari he huinga o ngā tohu fakamamahi tata toutou, kia me whakahaere tikanga tākuta i te maha o rite mate.

Roentgen faaore mohiotia Chondrodystrophy, hemihypertrophy wheua atrophy ranei, deformation rachitic me etahi atu mate. Hoki, e tika ana ki a X-hihi, kua araia reira mate Recklinghausen, e te nuinga o taea te raruraru mate Ollier. Ko te parau tumu matua - hiahia ki te mahi i te x-ray te kōhiwi katoa, nui atu i te wahi o reira.

Aratohu maimoatanga

Diskhondroplaziya i te kau, kāore, e kore tikanga kouma o te maimoatanga. I roto i te rerekē, hei tauira, pērā i mate rite hip dysplasia, chondromatosis tukinotia anake i te ako hāparapara o deformation. I roto i ētahi wā, whakaatu reira he whakakapinga huha tāwhaiwhai. Ko te toenga o te maimoatanga e kia riro te manawanui, - symptomatic me te tautoko.

tohua wawaotanga hāparapara te nuinga hoki ngā pakeke, mai, kia rite ki ngā tirohanga hou, ka kua te ako hāparapara i tau kura hua ōrite, e te tikanga e te tikanga o te maimoatanga hāparapara te anake i hanga i roto i deformation, engari e kore e hihiri. Heoi, i roto i whara nui pokanga taea mō ngā tamariki, tautautefito ki he taimi tae mai te reira ki te maihao, e e tino fakakehei i mate Ollier.

Ko te mate tā te whakaū tahi me te wheua: tūroro whakaaturia mau hu orthopedic, te whakamahi o Whītiki orthopedic me ētahi atu pūrere mō te whakatika hononga. me uru hangaia āta Tūroro mō tenei maimoatanga māuiuitanga me te mahi matatini hākinakina.

Whai hua rite taka porepore, me mahi i runga i simulators motuhake. E tauturu te reira ki te whakahoki te oro uaua, me te whakakaha i te mea tuhonohono.

outlook

E ai ki te rangahau, te nuinga o maha i roto i te pūhuruhurutanga o, te whakakapi wheua ngohe e wheua (pea e te aha i roto i te wā pakeke o te mate e kitea te tino uaua). Heoi, he iti iho i te raduzhen i roto i ngā tamariki taitamariki te matapae: deformation, ahakoa āta, engari kei te ahu whakamua. Ko tenei he aha te mea kino mate Ollier.

faaite te mate ake na takitahi i roto i ia take, e he uaua te waitohunga whānui ki te aromatawai unambiguously. A, no te pāpaka maha he reira atu pai atu i roto i te take o te whakarerekē paetata kotahi. arata'i deformation Takitahi ki te shortening o tetahi o nga wahi, me te i konei, i to ratou karawhiti, tautautefito ki he taimi tae mai te reira ki ngā tamariki iti. A e kore e taea ki te whakatika. i roto i te whanaketanga wawe o te mate pukupuku hoki faarahi te mōrea o ngā deformities o maihao.

Transformation ki chondrosarcoma

Ahakoa te meka e te hurihanga mārere i roto i te tirohanga - e kore e tupu maha, ano i reira he he tupono o te whakawhanake pukupuku - chondrosarcoma. Te nuinga tupu tenei i roto i te taiohitanga, ahakoa te maha o te rangahau o nāianei whakaatu e taea tupu te reira nui i muri mai. Hoki tenei take, e tūroro diskhondroplaziey körero auau ki te tākuta me te whakamātautau hauora tūtohutia.