Hauora, Diseases me ngā Here
Mate o Darier: take, tohu, maimoatanga
Te nuinga o te iwi, ko te tauira tangohia o ratou matua. riro tetahi nga kanohi puru o te popa, te tahi atu - makawe o whaea chic. O te akoranga, ētahi wā hurihia. Heoi, tupu tatou katoa ake hua ngā ira o to tatou whanaunga tata whatu. Tino maha, me kanohi nui, makawe mingimingi me te roa waewae, hoatu mau metua ratou tamariki i te huinga o rerekē mate. e kore te mahi e ratou i tenei i runga i whakaaro, ara kahore koutou ake whakaae. e kore e māuiuitanga tupu puta noa i te ora, engari atu maha he rerekē te āhuatanga. riro te tangata te purutia o mate utuafare me aorangia hoki. Ko tētahi o enei "mau horo'araa" he mate Darier. He aha te mea te reira? He aha ai tenei māuiuitanga?
mōhiohio whānui
I raro i pā te mate o Darier ki te dermatosis tuku whakakitea ponana i te puka o nodules parauri parauri ranei. He koeko-āhua, ka hipoki ki te parāoa matotoru ratou. Nodules paetata i runga i nga hipi tinana huihui mai, me te hanga i te patunga hou. Tei runga i te wāhi o te pāpaka, me to ratou ahua, e tahuri iho mate a Darier ki ngā puka e whā:
- Paetata. Āhuatanga e te whakaritenga rārangi o nga pokapū o e hipokina anake iti wāhanga o te tinana.
- Classical. Ponana nuinga paetata runga i te tumuaki, uma me taringa.
- Taratahi. Me puta nodules paerewa papules polyhedral Ahakoa kiritona. Tikanga, Ko ratou i runga i te hoki o nga ringa, me te waewae.
- Vesicular-bullous. Ko te tino onge tenei ahua o te mate. Kei te āhuatanga i te reira e te pāpaka maha ki te ngaro mārama. puta ratou i te taha o te kaki, i roto i te rohe o te hipi kiri nui.
E pāngia pāpaka Paraimere papules i roto i ngā tūroro i waenganui i nga tau o waru ki te tekau ma rima nga tau. aro ma'i Pakeke uaua.
Ko te take o te mate
Ko te take matua o tenei mate ko te aroaro o ira rerekē, me te āhuatanga mōrearea nui - predisposition riro. Ka rite ki te hua, e kore te huaora A tino riro e te tinana, heke te mahi o etahi whākōkī me ihirangi konutea i roto i te kiriwaho te. Ko te putanga o enei tukanga pathological ko te takahi o te huarahi o te keratinization kiri.
Ki te mama papa ranei he kawe o te ira rerekē i roto i te 50% o te wā, puta te marama he tamaiti ki te tātaritanga o "mate a Darier." Heoi, ki te whanau te tūroro mātua tamaiti tino hauora, tenei māuiuitanga e kore te whakararuraru i ana tamariki ake nei. E kore te te mate tuku e rūrūtia mahino moepuku ranei.
pikitia haumanu
haamata te tukanga pathological ki te ahua o nodules follicular flat, e e te kore mohiotia rite papules. kia rerekē ratou rahi i te 1 ki te 3 mm. Papules hipoki ki te kirinuku mārō o te tae parauri. I raro i reira i reira he depressions i te āhua o te kōrere. E kei Nodules i nga mangai o follicles makawe, e te tahi mau taime e arata'i ki te whanaketanga o tetahi mate - folliculitis. Na reira, i mua i tīmata maimoatanga he tika ki te whakahaere i te tātaritanga pārōnaki.
E whakaritea hūnga symmetrically Wairaka ki rohe subclavian me nga papa flexor o te hononga iho. I runga i te tumuaki papule haamana'oraa whakatū papa warty patito ki parāoa. I muri ratou tango i roto i nga wahi o pāpaka puta aronga o alopecia. Ka rite ki te mate kauneke reira he rashes hou, me te hanumi tawhito ki te wahi kotahi.
whakamātautau Medical
hāngai ana tātaritanga o te mate kei runga i te pikitia haumanu, me te hītori oti hauora o te manawanui. I roto i te whakamātautau, tirohia te tākuta te tohu o te mate, take mua o rashes roto whanaunga tata. Hei whakaū i te mate whakaritea te he tātaritanga histological o unuhanga kiri. kawea te tātaritanga pārōnaki te roto ki te pemphigus te utuafare,, papillomatosis me dermatitis seborrheic.
te mau parau tumu therapy
Maimoatanga ki tenei raruraru te tikanga whakamana i runga i te kaupapa tūroro. I roto i exacerbation o te tukanga pathological puta titau whānui manawanui pāpaka hohipera i roto i te hōhipera Dermatological ranei.
Ko te manawanui ko te therapy symptomatic. tūroro katoa ki kahore he okotahi whakaritea huaora A i roto i te puka o te werohia-waha intramuscular ranei. tatau Inenga Kei te takitahi, tango ki pūkete tau o te manawanui. Ko te nuinga o 3 marama te akoranga o te maimoatanga, ka meinga he whati, me te faahiti i te maimoatanga.
He hua pai ki te mate Darier hoatu mirumiru pati i roto i ngā ki tono hinu keratolytic. I roto i te aroaro o pāpaka nui, wawaotanga hāparapara electrocoagulation ranei. A, no te tahi mate o Darier e te tua o te whakapokenga huakita, whakaritea he rongoā paturopi te.
Matapae me te ārai
tuku te mate e anake e tupu. Ko Ko te aha rite he tohunga ārai tuatahi tūtohu kōrero ki te geneticist ki faaipoipo whakamahere i roto i te wa e tata ana hapu te tamaiti. Ko rawa pono o te mau metua, e i roto i te utuafare, kua oti kē te pāngia ki te mate o Darier tenei.
Te maimoatanga whakaahuatia i runga, te tikanga whakaatu hua pai. Ka taea e maha tūroro whakatutuki tu murunga mo te tau torutoru. Heoi, e kore e kotahi e mahara i te ora tonu.
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