Hauora, Diseases me ngā Here
Pancytopenia - he huru pathological i roto i nei heke i roto i te toto komuhumuhu o ngā āhuatanga katoa o te hanganga. Take, tohu, maimoatanga
Tetahi whanaketanga o te mate i roto i te tinana ai te huringa i roto i te mahi i te toto piringa. Heoi, i reira e he maha o pathologies mo e he taua rerekētanga te āhuatanga haumanu matua. Pancytopenia - Ko tetahi o nga tukanga pathological o te pūnaha hematopoietic, tautuhia nei te rite te mate motuhake, ranei kia te faaiteraa o te tahi atu te rere nosological.
ariā General
E kore te mea noa te mate, na e kore te nuinga o te iwi e mōhio o te tītohunga taua. Pancytopenia - he āhua o te hē o ngā pūtau toto, meinga te whanaketanga o nei e abnormalities i roto i te hanganga o ngā pūtau toto kawainga i te wā o te hematopoiesis. taumata iti o ngā pūtau whero toto, ma pūtau toto me platelets tika ki te meka e kore e taea e te pūtau kakau āta mahi.
whakawhanake te mate i roto i ngā puka e rua:
- idiopathic, meinga e ngā āhuatanga ā-;
- Tuarua, meinga nei e awe waho.
He huru pathological i roto i pā ana ki 50% o ngā take whakawhanake momo autoimmune. Ko, kei te whawhai anake te tinana ki o koutou pūtau toto, pōhēhē ratou hoki māngai ke. puka Idiopathic taea whakatika ki tāpiritanga o atu take waho e whakatere te putanga kino.
Pancytopenia - he mate e taea te riro, te whakawhanake i te wa, ka ko te tamaiti i roto i te kopu. whanau he tamaiti te kua ki disorders o nga whekau toto-hanga. Ka taea e te reira congenital me wheua wheua hypoplasia, kia e kore e taea e te pūnaha akakoromaki i to ratou mahi.
Ko te etiology o nga āhuatanga mate me te mōrea
I roto i te take matua o te whanaketanga o te mate he irakētanga ira, te whakamahi wā roa-o taero, iraruke ranei pānga paitini. āhuatanga puka Idiopathic e te meka e kore e taea te whakapumautia te take, Heoi, i reira nga take o te mate i muri i te whanautanga tamariki.
Te Haamauraa i te take he mea nui hoki te putanga pai. Whakakore i te mana kino waho i roto i tenei mate - 50% auau angitu.
I tua atu ki te take matua i reira e rave rahi āhuatanga e whai wāhi ki te whanaketanga o te māuiuitanga:
- Mahi ki benzene te ateneke ranei;
- anemia Fanconi;
- te āhua viral o te mate;
- hahau;
- paturopi me immunosuppressants;
- mate autoimmune pērā i erythematosus lupus pūnahanaha;
- iraruke.
anemia Fanconi - tetahi o nga āhuatanga etiological o pancytopenia. Whanake i runga i te whakamārama o kōhikohiko congenital whakaaro te he mate ngoikore autosomal. āhuatanga anemia e te aroaro o mea kohakore i wahi o te pūmua haepapa mō te DNA hanga me te pūira friability.
Ko te pikitia haumanu o te mate
faaite huru pathological ake i roto i te puka o te toru syndromes. Ia o enei āhuatanga āhuatanga ki te whakaiti i te maha o tetahi momo o ngā pūtau toto. whakaaturia Leukopenia te he pikitia o te sepsis whakapeka, me te putanga o ngā tukanga whewhe-necrotic o te kiri, me te kiriuhi mucous.
Erythropenia me whakaiti i tohua i roto i te pūtoto whakapataritari i te whanaketanga o nga tohu o te anemia. āhuatanga tēnei āhua e:
- koma o kiri integument;
- rere i mua i ona kanohi ;
- whanoke;
- tinnitus;
- ngoikore me te rohirohi;
- ngoikore.
amuamu Tūroro o te mamae o te manawa, me te ngakau palpitations. Auscultation ki te whakatau pepe ngakau reokore, amuamu systolic i runga i te mata katoa o te ngä ngakau, te haruru o te tihi o te rua jugular. Te ähua o te huru o te manawanui ai huringa i roto i te hiko-, e tohu te whanaketanga o te kore ngakau.
whakakitea Thrombocytopenia e auau toto (epistaxis, gastrointestinal, uterine), te toto pae, te ahua o te petechiae me pakaruhanga toto i roto i te kiri. puritia tohu whakapeka o te mate e hoki e pā ana ki te marama, me te maha arahi ki te mate. tukua pancytopenia ma'i atu pai, me te kua he tohumate iti korerotia
whakaaro te mate te ki kia hoki rawa matatini. Pancytopenia, e he atu noa mō te iwi paari pōauautanga, tahi e te ahua o te mate, me te toto.
mehua tātaritanga
titau te take tuatahi tuku ki te tirohanga mātanga, hītori kohinga me te ora o te manawanui. I tua atu i whakaritea CBC. I roto i te take o enei tohu e taea whakaata i runga i te whanaketanga o te pancytopenia me whakahaere mehua atu tātaritanga:
- leukocytes <2 x 109 / l;
- platelets <150 x 109 / L;
- erythrocytes <3,5 x 109 / l.
Whakaritea ako poka wheua wheua, e tautuhi ana i te aroaro o ngā pūtau rerekē me myelokaryocytes. Whakaritea e te aroaro o abnormalities, tae atu wheua wheua hypoplasia. puritia hoki tauira hemolytic.
maimoatanga pancytopenia
takahanga haumanu whakawhirinaki i runga i te take haumanu, huru o te manawanui, me te take etiological e meinga te mate. Ka taea te whakamahi i te tikanga maimoatanga e whai ake nei:
- Toto huhu, ki te taurite te toenga o ngā huānga puka.
- Transplantation o wheua wheua kakau ranei pūtau. E mea pinepine whakamana i roto i te tūroro taitamariki, me te waenganui tau.
- I roto i te take o te pancytopenia autoimmune whakahaerea tono immunosuppressant "Cytoxan", "Methylprednisolone," "Neoral", "Sandimun".
- Tikanga whakaongaonga i te hinu wheua wheua ki te mahi - "Neupogen", "Neulasta", "Procrit", "Leukin".
tipu tarukino
Ko te therapy mate matatini ngā te whakamahi o te rongoā. Ka taea te whakaarahia te taumata o ngā pūtau toto whero, me te pūtoto ki te awhina o hua. E hanga teas taiepa i runga i te pūtake o te pungarehu, currants mangu, whakatika hope, rōpere, hua, aperikota. Rino taonga keha, gooseberries, Cherries me karepe, te kai o e kore e pauna anake te toenga o ngā pūtau toto, engari whakakaha ano hoki te pūnaha ārai mate.
Kei roto te maha o ngā tikanga tangata mō te rongoā pancytopenia honi. Kei te ngā reira ki te hua e whai ake nei:
- ki te waina whero, me te aroe;
- karika;
- ōti;
- rēmana, āperekoti maroke, karepe, maha me wōnati.
Āpiti faufaa nui ki infusions me decoctions o otaota rongoa Ongaonga Ongaonga, birch, tarutaru paari, clover, aihere, tāwhara, clover, Buckwheat.
mutunga
Pancytopenia - he mate nui, e rite ana ki te mate whakamate. Tei putanga pai i runga i te pakeke o nga tohu haumanu, puka, me ngā wāhanga o te whanaketanga i roto i i tīmata maimoatanga. Ko māmā ki te ārai atu i ki te rongoa taua mate.
Ko te whakamātautau hauora ā-tau o te taupori whai wāhi ki te tāutu o te huru pathological i roto i te tīmatanga o te wāhanga. I roto i ngā pā tenei ki tikanga taiwhanga whakamātautau.
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