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Polycythemia - polycythemia ko ...: Tohu me Treatment

Polycythemia - he mate tena i ai piki ihirangi pūtau toto whero (pūtau toto whero) i roto i te toto. Ano, ka he māuiuitanga taua i roto i 70% o ngā tūroro rerekē te maha o platelets me leukocytes i roto i te ara nui.

E kore e te mate i te nuinga nui - tau ia miriona taupori rēhita kaua e nui ake rima taime. Nuinga o ngā wā whakawhanake te mate polycythemia waenganui-koroheke, me te iwi kaumātua. E ai ki ngā tatauranga, he mamae tane tenei mate e rima nga wa atu pinepine atu i te wahine. I teie mahana, e whakaahuatia te titiro i tenei ahua rite polycythemia, tohu me te maimoatanga o mate i raro.

Ko te take o te mate

Polycythemia - he mate kore-mārere. Ki te rā, te take tangohia o te mate ko te unknown. Kei te whakapono te reira e te mate e meinga e irakētanga whakawhanake whākōkī wheua wheua motuhake. huringa ira arahi ki wehenga nui, me te tupu o ngā pūtau toto, ngā pūtau toto whero.

whakarōpū o mate

E rua ngā rōpū o te mate:

  • Polycythemia Vera ranei mate Vakeza, e te roto i te tahuri wehea ki te tuatahi (i.e., mahi rite he mate motuhake), me te (whakawhanake polycythemia tuarua e tika ana ki mate pūkahukahu ma'i, te pukupuku, hydronephrosis, i runga i te ara tiketike) tuarua.

  • polycythemia pātahi (ahotea teka ranei) - ki te ko tenei āhua te taumata o ngā pūtau toto whero i roto i te whānuitanga noa.

Polycythemia: tohu o te mate

Tino maha, he asymptomatic te mate. I te tahi taime, ka rite ki te hua o te rangahau mō ngā take rawa rerekē kia reira aitua whakakitea polycythemia. Tohu, kia e whakarongo, titiro i muri.

Roha o uaua subcutaneous

A, no te polycythemia i runga i te kiri, tino maha i roto i te kaki, whakaatu dilated uaua subcutaneous i roto i. Ki tenei mate riro te kiri tae here whero, rawa kite i roto i te tuwhera ngā wāhi o te tinana - kaki, ringa, mata. Ko te kiriuhi mucous o nga ngutu, me te arero, ko te tae kikorangi-whero, toiwhenua o nga kanohi te titiro whero.

ai te reira i huringa i roto i te waipuke toto taonga i roto i erythrocytes, oko mata katoa me tērā ona āhuatanga rheological (tere o ngā), i runga nei te wahi matua o te pūtoto (ngarahu whero) riro te puka iti (i.e., te whakamamaetia huringa matū) me huringa tae.

apohia e

Tata hawhe o nga tūroro mate i te polycythemia, i reira te mea he apohia e kaha, tino kitea i muri i tango i te pati mahana. tavini ana tēnei āhuatanga rite te huru motuhake o te polycythemia Vera. Puta tika ki te tuku o matū kaha i roto i te toto, i roto i te histamine ngā, i te mea e taea ki te whakawhānui i te tōiti kiri, ārahi ki nui haere rere toto i roto i a ratou, me te ahua o sensations motuhake waihakihaki.

Eritromelalagiya

āhuatanga tēnei āhuatanga e te mamae wā-poto kaha i roto i te matimati. Whakaoho ratou taumata mōtepe hua i roto i oko iti o te paraihe, hua i roto i te hanganga o te maha microthrombuses, arterioles tūhonoa me te ārai rere toto ki nga kopa o te maihao. āhuatanga waho taua huru he whero me te ahua i runga i nga wahi kikorangi kiri. Hoki te whakaaro o te ārai Thrombosis ahipirini tūtohutia.

Splenomegaly (whakarahi o te kōateate)

Haunga te takihi, ate, e taea, ka puta ke, ranei, kaua tona rahi. E whai wāhi tika enei tinana i roto i te hanganga me te whakangaromanga o ngā pūtau toto. Te whakanui ake i te kukū o te ahu muri ki te hua i roto i te ate, me te kōateate.

mariao Duodenal me te puku

whakawhanake taua māuiuitanga hāparapara mamae e tika ana ki te oko Thrombosis wahi kūnatu membrane iti mucous. Ko te hua o te whakapeka disorders circulatory he necrosis (necrosis) wahi taiepa tinana, me te hanga i tona pae o te whewhe. I tua atu, heke ātete ki helicobacter pekitīlia (he moroiti meinga whewhe me gastritis).

clots toto i roto i te oko nui

He atu e pängia ana ki tenei mate o te uaua e alangá raro. Thrombi, whawhati atu i te taiepa oko e taea, bypassing te ngakau, kia tomo ki roto ki te tohanga pūkahukahu (pūkahukahu) ka meinga Embolism pūkahukahu (Embolism pūkahukahu) - he huru hohotahi ki te ora.

te toto pae

Ahakoa te maha o platelets i roto i te toto piringa rerekē me whakanuia ana tona coagulation, kia puta toto gingival ka polycythemia.

kauti

I ngā taumata teitei o tai waikawa uric ona e takoto i roto i ngā hononga, me te whakapataritari i te mamae koi.

  • Mamae i roto i te wahi. Tenei tohu ai pera waewae kino, whāiti ratou me, rite te tupu, te tohanga rawakore. huaina ana tēnei māuiuitanga ko "mate occlusive"
  • Mamae i roto i te wheua flat. Nui haere mahi wheua wheua (wāhi whanaketanga o ngā pūtau toto) whakaongaonga te tūtohutanga o wheua flat ki ahotea aunoa.

Ko te ino o te huru whānui o te kaiao

I roto i te mate pērā i polycythemia, kia rite ki ngā tohu o ētahi atu disorders (hei tauira, anemia) tohu: pāhoahoa, rohirohi tamau, tinnitus, te taninito, e rarapa "mania" i roto i te mua o te kanohi, hāhā o te manawa, toto ki te matenga. āhuatanga pokey toto nui haere whakahohetia oko tauhohenga e vai, rite ki te hua, i reira he he hua i roto i te pēhanga toto. A, no te maha i tenei mate pōauautanga pērā i te kore ngakau, me te mikrokardioskleroza (whakauru o kiko tūhonohono o te uaua ngakau, whakakiia te koha, engari e kore e mahi i te mahi e tika ana).

tātaringa

Polycythemia whakakitea nga hua o te tātari toto whānui, i kitea:

  • maha nui o ngā pūtau whero i 6.5 ki te 7,5 • 10 ^ 12 / l;

  • taumata teitei o te pūtoto - 240 g / l;

  • ngeniwhero katoa (OOE) nui 52%.

Mai kore e taea te tatau te maha o ngā pūtau toto whero i runga i te pūtake o te uara ine i runga, whakamahia hoki ine tātaritanga radionuclide. Ki te te papatipu o ngā pūtau toto whero he nui atu i 36 ml / kg i roto i nga tangata, me te 32 ml / kg i roto i nga wahine, i te reira tika tohu te aroaro o te mate Vakeza.

A, no te puritia polycythemia te Morphology o ngā pūtau toto whero, arā, e kore ratou e taui i to ratou āhua noa, me te rahi. Heoi, ki te whanaketanga o te anemia tika ki toto nui bleedings auau microcytosis kitea ranei (heke pūtau toto whero).

Polycythemia: maimoatanga

pānga haumanu pai he e totó ko. Tūtohutia wiki 200-300 ml o toto i nekehia atu ra ano OOE tae noa ki makaka te taumata ki te uara e hiahiatia ana. Ki te mea i reira he contraindications mo e totó ko, whakahokia he taea i te tikanga o waimehatanga toto te ōrau o ngā pūtau toto whero mā te tāpiri i te wahi wai (e whakahaere rongoā macromolecular pâmuhia).

kia whanau te reira i roto i te ngakau e tino maha te toto ahu ana ki te whanaketanga o te rino hē anemia i roto i nei i reira e hāngai tohumate me te hua i roto i te tatau mōtepe.

Ki tenei mate rite polycythemia, titau maimoatanga tautukunga ki etahi kai. E tūtohutia ana ki te whakawhāiti i te kohi o te kai, me te ika hua, kia rite ki roto i ratou he nui tiketike o te pūmua, whakaongaonga te mahi o te toto. kia hoatu ano hoki e koe ake nga kai fatty. whai wāhi cholesterol ki te whanaketanga o te te atherosclerosis, meinga thrombi, i roto i ngā rahinga nui, me te pera e hanga e i roto i te iwi e mate ana i te polycythemia.

Ki tenei mate, e tūtohu ana ki te hoatu hiahia ki te miraka me te whakato hua, a ki te whakawhāiti mahi tinana.

Hoki, ki te pāngia rite "polycythemia", kia ngā maimoatanga hahau. Faaohipa i te reira i te thrombocytosis teitei, me te minamina kino. Tikanga, tenei "kaihoko cytoreductive" ( "Hydroxycarbamide" teuteu).

Tae noa tata, i roto i te tikanga ki te pehi wheua wheua werohia o kanoirite iratuki whakamahia (nuinga, ūkuikui-32). I teie mahana, piki kore taua maimoatanga no o te auau tiketike o te huringa leukemic.

Therapy hoki ngā werohanga o interferon mo te maimoatanga o te thrombocytosis tuarua whakamahia tarukino "Anagrelide".

I roto i tenei mate kua uaua whakamana wheua wheua transplantation, mai polycythemia - te mate e kore ko e mate, whakaratohia, o te akoranga, rawaka maimoatanga me te aroturuki tamau.

Polycythemia i roto i whanau hou

Polycythemia - he māuiuitanga, nga tohu o e taea te kitea i roto i whanau hou. Ko te mate, ko te whakautu o te tinana ki te kongakonga hypoxia whakawhiti, e taea e whakapataritari iti hoki placental. te tinana ki te whakatika i hypoxia haamata pēpē ki synthesize he maha nui o ngā pūtau toto whero.

I tua o te romahā makatuunga, kia whakawhanake i te hou, me te polycythemia Vera. Taua mōrea e ngā puhoi wāhi mahanga.

Polycythemia i roto i te hou whanake i roto i te torutoru wiki tuatahi o te ora, ko reira te faaiteraa tuatahi o te hua i roto i te hematocrit (60%) me te hua nui i roto i ngā taumata pūtoto.

He maha ngā wāhanga rere polycythemia fā'ele'i: tuatahi, taahiraa poliferatsii me te rohirohi. whakaahua poto ratou.

He tata kahore tetahi faaiteraa haumanu te wāhanga tuatahi o te mate. Polycythemia whakakitea te tamaiti i tenei wā, ko te taea anake e rangahau o toto piringa: hematocrit, taumata pūtoto, me ngā pūtau toto whero.

I taahiraa poliferatsii whakawhanake he ate rahi me te kōateate. kite Pletoricheskie ari: te kiri whiwhi i te āhuatanga "pletoricheski whero" hue, whakaatu ana te tamaiti manukanuka, ka pa ki te kiri. Pletorichesky syndrome kīnaki Thrombosis. Ko te tātaritanga o te huringa kitea i roto i te maha o ngā pūtau toto whero, platelets me huringa leukocyte. kia hoki kia nui haere Tohu o ngā pūtau toto, ka karanga te tītohunga taua te "panmieloza".

āhuatanga Hipanga kēkeno e mate taimaha nui, asthenia me te rohirohi.

Hoki huringa haumanu hou taua tino taimaha a taea whakapataritari huringa tina heke, me te mate i muri. kia Polycythemia he hara o te whakawhanake i te tetahi momo o ngā pūtau toto ma e he kawenga mō te pūnaha ārai o te tinana. Ka rite ki te putanga, whakawhanakehia te tamaiti mate nui o te natura kitakita, ārahi te mutunga ki te mate.

I muri te pānui i tēnei tuhinga, ka ako koe atu e pā ana ki tenei mate rite polycythemia. i whakaaro e rite nui tatou taipitopito rite taea tohumate me te maimoatanga. Te ti'aturi nei tatou i te mōhiohio homai e kia whai hua ki a koutou. Kia tupato o koe, ka noho hauora!

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