HauoraRongoā

Pūkahukahu Vienna. uaua pūkahukahu Anomalous

Pūkahukahu Vienna (pikitia whakaaturia ana i raro) - he oko e hopoi mai ia toto te toto taonga e ki te hāora i roto i te pūkahukahu ki te marae i mahue.

Tīmata i te tōiti pūkahukahu, hanumi nga oko ki uaua nui, e kua tonoa ki te bronchi, a ka wāhanga nga hea, a ka he ngāwari te kuwaha ki te hanga i te kahiwi nui (e rua i ia o te pakiaka), i te mea i roto i te tūnga whakapae e tonoa ki te wahi o runga o te marae i mahue. I tua atu, i ia o nga oko, tomo ki te kohao motuhake: mahue - i te taha ki maui o te marae i mahue me te tika i te tika. uaua pūkahukahu Matau, e whai ake nei e Atrial (maui) transversely whakawhiti te marae tika (tona hoki).

pūkahukahu waho (tika) Vienna

I hanga wāhanga rua segmental o nga matamata pūkahukahu waenganui, me te runga.

  • R.apicalis (apical peka) - kanohi kātua venous poto, kei nei i runga i te taupa o runga (mediastinal tona mata), me te waha ana toto i te matamata wāhanga. I mua i tomo ki roto ki matau te iahoki pūkahukahu pai pinepine ngā ki segmental (muri) manga.
  • R. posterior (peka muri) te maua e kohinga toto i te wāhanga muri. Tenei peka - te nuinga o nga uaua katoa nui Vienna (segmental), e kua kei roto i te taupa o runga. I roto i tenei oko he taratahi e rave rahi wahi: wāhanga poddolevoy vnutrisegmentarny me te wāhanga e kohikohi toto i interlobar wāhi mata o Kosi matahao.
  • R.anterior (peka mua) te maua e toto i te wahi kohikohi o runga (wāhanga mārōrō ranei). I roto i ētahi wā, ka taea ki te whakakotahi i nga manga mua, a muri (ki te taka ratou ki roto ki te kātua noa).
  • R.lobi medii (peka taupa waenganui) e tango toto i te wāhanga pūkahukahu tika (tona wahi toharite). I roto i ētahi wā, e tenei te ahua o tetahi Vienna oko, me te rere ki runga te iahoki pūkahukahu tika, engari maha i hanga mauanga te o rua nga wahi: ko te medial me lateral e tatau aua wāhanga medial me lateral.

pūkahukahu raro (tika) Vienna

Tenei oko e te toto i te taupa o raro (ona wāhanga 5), me te e rua whiwhinga matua: rua basal me peka runga noa.

Ko te peka o runga

takoto te reira i waenganui i te basal me wāhanga o runga. Kei te hanga e i te atu, me te matua uaua, kia kia mua, ka ki raro, haere i muri i te ngōrahi segmental apical. Tenei peka Ko te tihi o katoa e kau ki te raro iahoki pūkahukahu tika.

Fakatatau ki ai Bronchitis Vienna ngā toru whiwhinga matua: lateral, medial runga, kei roto i te nuinga o te intersegmental engari ka taea e rere me te vnutrisegmentarno.

Nā ki te atu rua toto matamua kawea e runga i te wāhanga (tona runga) i roto i te rohe poddolevuyu segmental rua muri taupa o runga (tona wāhanga posterior).

Basal katoa Vienna

Ko te kātua venous poto, i hanga i te komititanga o nga uaua o raro, me te runga basal manga matua e takoto mata noa hohonu mua.

Basal tihi Vienna. I hanga i te taha o te hanumi, o te nui rawa uaua segmental basal me uaua e kawe te toto i te medial, mārōrō me wāhanga lateral.

raro basal Vienna. Āpitihia ki te rua basal whānui i tona mata hoki iti. Ko te Päkehä ki matua o te ipu - manga posterior basal e kohikohi toto i wāhanga posterior basal. I roto i ētahi wā, ka taea e te raro basal Vienna whakatata te tihi o te rua basal.

ADLV

Ko te mate ngakau congenital i ai kitea takanga te neanatomichnoe uaua pūkahukahu ki te marae (tika), whakaurua ranei i te hou o te iahoki vena cava.

haere tahi ana tēnei māuiuitanga e kakā auau, te rohirohi, hāhā o te manawa, roa o te whanaketanga tinana, te mamae cardiac. Ka rite ki tātaritanga kua whakamahia: ECG, MRI, X-hihi, catheterization cardiac, ultrasound, me atriografiyu ventrikulo-, angiopulmonography.

Tei hāparapara koha maimoatanga i runga i tona momo.

Overview

ADLV - koha congenital me ko e pā ana ki 1.5-3.0% o mea kohakore ngakau. Te nuinga o te kitea i roto i te tūroro toa.

Nuinga o ngā wā ngā tenei koha te ki te porotītaha (tuwhera) matapihi me hē pātaki i waenganui i nga ventricles. Paku iti (20%) - i te toto kātua noa, hypoplastic taha maui o te ngakau, VSD, dextrocardia, tetralogy o Fallot, me transposition o nga oko nui, ana roro ngakau whānui.

I tua atu ki enei kohakore, maha haere tahi ADLV extracardiac māuiuitanga: hernias pito, mea kohakore i roto i te wheua hanganga me ngā pūnaha endocrine, diverticula intestinal, tākihi hūhoiho, mate tākihi polycystic me hydronephrosis.

Classification anomalous pana wai venous pūkahukahu (ADLV)

I roto i te take o te pūruatanga o te uaua i roto i te tohanga nahanaha ranei ki te marae tika, ka karanga i tenei koha ko te waikeri anomalous tonu, ki te i roto i te hanganga i runga rere ki tetahi he torutoru uaua ranei, ka karanga he koha taua te kanohi.

I roto i runga ki te taumata o te kongutu tohatoha etahi kōwhiringa kohakore:

  • kē Tuatahi: nadserdechny (suprakardialny). Ko te uaua pūkahukahu (pērā i te kātua noa motuhake ranei) rere ki te iahoki vena cava runga ona manga ranei.
  • Kōwhiringa e rua: ngakau (intracardiac). uaua pūkahukahu ringihia ki te pakohu coronary te marae matau ranei.
  • Whakatinanatanga Tuatoru: podserdechny (pōkākā subcardial ranei). tomo uaua pūkahukahu te tomokanga vena cava ranei iahoki raro (nui iti i roto i te tau mahani lymphatic).
  • Ko te kōwhiringa tuawha: konatunatua. ngā uaua pūkahukahu i roto i ngā hanganga rerekē, me te i ngā taumata rerekē.

āhuatanga hemodynamics

I roto i te utero kore te nuinga o te kite koha kaha, no te mea o te peculiarities o tohatoha fetal. I muri i te whanautanga o te tamaiti e tautuhi faaiteraa hemodynamic mō tenei koha me tona huinga ki ētahi atu kōhikohiko congenital.

I roto i te take o te katoa pana wai anomalous o disorders hemodynamic faaite hypoxemia, kikī hyperkinetic o te ngakau tika me te takawhita pūkahukahu.

I roto i te take o hemodynamics pana wai wāhanga rite ki taua ki ASD. Ko te tūranga ārahi no ki te maumaui o whakanekeneke arteriovenous rerekē, e arata'i ki te hua i roto i te rōrahi toto i roto i te porohita iti.

Tohu o anomalous pana wai venous pūkahukahu

maha Kids ki tenei koha mamae recurrent whakapeka mate viral matehā me kakā, mea ratou mare, iti taonga taimaha, tachycardia, hāhā o te manawa, mamae ngakau, cyanosis marama, me te rohirohi.

I roto i te take o te takawhita pūkahukahu he kitea i roto i te tau iti puta kore ngakau, ua faaite cyanosis me te koropuku ngakau.

tātaringa

auscultation Pikitia i ADLV rite ki ASD, e ko te hanganga iu haruru systolic auscultated i te haurangi o uaua pera (uaua pūkahukahu) me te wāwāhi o te reo 2.

  • Ko te tohu ECG o kikī ngakau tika, nga EOS ine pā matau (oti), tika paihere poraka manga.
  • A, no te tohu phonography o ASD.
  • I roto i te Radiography riro marama tauira kua ngawha iatuku pūkahukahu (tona pewa), whakawhänui tika nga rohe cardiac, "Turkish saber" tohumate.
  • Echocardiography.
  • To'na iteraa kōwhao cardiac.
  • Venography.
  • Atriografiya (tika).
  • Angiography.
  • Ventriculography.

kia whakamana te tātaritanga pārōnaki o tenei koha:

  • Lymphangiectasia.
  • atresia te pūtahi o / piha mitral.
  • oko transposition.
  • stenosis Mitral.
  • Stenosis o te matau / mahue uaua pūkahukahu.
  • Trehpredserdnym ngakau.
  • ASD taratahi.

maimoatanga

Ngā momo o te pokanga pana wai wāhanga whakaritea e tetahi koha, te rahi me te wāhi ASD.

whakakore karere Atrial whakamahi kirihou suturing ranei ASD. Kohungahunga ki runga ki te tau o te toru e te hunga i roto i te huru fifi tino, te kawe i roto i pokanga whànau (atrioseptotomiyu kati), e hāngai ana nei i whakawhänui kōrero interatrial.

Tapeke ako koha tuwhena (ngā tapeke) ngā maha ngā whawhe.

  • Ligation pou pathological uaua iaia.
  • Wehe o nga uaua pūkahukahu.
  • Katinga o ASD.
  • Anastomosis i waenganui i te marae i mahue me uaua pūkahukahu.

Ko te putanga o taua ngā mahi kia: hua o te syndrome takawhita pūkahukahu me te kore pakohu kōpuku.

matapae

mate te waitohunga o te akoranga tūturu o tenei koha kino, mai 80% o tūroro i roto i te tuatahi o nga tau o te ora.

Tūroro ki te aroaro o te waikeri wāhanga taea ora ake ki te tau o te toru tekau. Ko te mate o taua tūroro te tino maha e pā ana ki mate pūkahukahu, kore nui ngakau ranei.

Hua o te ako hāparapara o te koha maha pai, engari i roto i te lethality fā'ele'i i roto i muri i te mea tiketike tafa ranei.

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