HauoraRongoā

Tauhohe Leukemoid i roto i ngā tamariki: te momo (momo), take, te tātaritanga Hātepe maimoatanga. tauhohe Leukemoid me kanisā: ngā rerekētanga

tauhohenga Leukemoid - taui hematopoiesis, rite ki te pikitia toto i roto i te kanisā, me ētahi atu pukupuku o te pūnaha hematopoietic. Me kï reira e te pū o enei pānga ko to ratou takotoranga kaha, me te kore o te whakawhitinga i roto i te mate pukupuku. Ka taea te pōreareatanga e ngā momo intoxications, pukupuku, mate, mate pukupuku roro metastatic ēnei tauhohe.

Tikanga o te whanaketanga rerekē ki te momo rerekē o tauhohe: i roto i ētahi wā he mea putanga i roto i te teeki huānga pūtau toto, i roto i etahi atu - nui haere production o ngā pūtau toto ranei here o ngā pūtau putanga i roto i te kikokiko, ranei te aroaro o te maha pūhanga wā kotahi.

He aha i taea e te puna o te mate?

He maha ngā āhuatanga e kia puta tika te tauhohenga leukemoid. Ngā take mō ratou whanaketanga e:

  • mana o ionizing radiation;
  • kohi;
  • sepsis;
  • tukanga purulent;
  • koripi;
  • mate o Hodgkin;
  • whētuki cranial;
  • ru;
  • lobar kakā;
  • erysipelas;
  • diphtheria;
  • ngangana kirika;
  • ma'ii'o ate whakapeka;
  • therapy corticoid;
  • waro paihana hāoratahi.

mate momo

Ko nga momo e whai ake nei o tauhohe leukemoid:

  • tauhohenga Myeloid.
  • Lymphocytic.
  • Psevdoblastnye.

Kia whakaaro tatou ia o ratou i roto i ngā kōrero.

myeloid

Na roto i tenei momo o te tauhohenga ngā pērā i neutrophil, eosinophil me promyelocytic. pānga Leukemoid rite ki te hunga o te kanisā myeloid ma'i, tahi e haurangi me mate kino. leukocytosis Active he tukanga uaua tahi e te aroaro o sepsis, aronga inflammatory me nui haere te pāmahana tinana waiwai tonu.

Mārakerake i roto i te taikaha o eosinophils i roto i te toto ahu ki te puta, ka sensitization ki te werau me taero, diathesis mate pāwera, uaua - i mate oncological (mate o Hodgkin me lymphosarcoma). Ēnei tauhohe leukemoid Me hoki te rangahau whānui ki mate wāhitau o te pūnaha circulatory, me kutukutu.

pūtau Urupare rite eritremii. āhuatanga polycythemia - ko te hekenga i roto i ma'i pūkahukahu oxygenation (oxygenation) te toto, te pukupuku tākihi, me te mate ngakau congenital maha. Me whiwhi tēnei āhuatanga he rorohiko me te ultrasound.

Mielemiya rite ki erythroleukemia whakapeka, e rerekē anake i roto i te kore o te hau erythrocytes i wheua wheua, me te toto. E mea pinepine te mea e taea ki te kitea metastases i mate wheua.

lymphocytic

Kei te āhuatanga e te hua nui i roto i te katoa maha o lymphocytes i toto piringa, i te mea maha kawenga mō te hua i roto i te ate, taikiri me te kōateate ēnei tauhohe.

Ki tenei momo no mononucleosis, hopuhopu lymphocytosis, tauhohe leukemoid monocyte-macrophage i roto i ngā tamariki ki te mate kitakita me te viral, me mate Parasitic me te toto tiketike eosinophilia (hei tauira, helminthiasis).

tauhohe Lymphocytic puta:

  • mate viral (koroputa, kōpukupuku, repe, mate adenovirus, karawaka, mononucleosis hopuhopu);
  • mate pirinoa (rikketsiozah, toxoplasmosis, chlamydia);
  • mate kitakita (pakewakewa, pertussis, kohi);
  • ngā mycoses;
  • mate autoimmune (mate serum, pūnahanaha erythematosus lupus).

momo Lymphocytic atu noa i roto i macroglobulinemia Waldenstrom, mumura, sarcoidosis. Kua tukinotia katoa o te ma'i i runga rawa tino a taea e huanane mo te manawanui atu i te tau.

Psevdoblastnye

E leukemoid taua tauhohe ki te kei te timata anake te manawanui ki te puta i te agranulocytosis ārai, te take o e taea te pōreareatanga i fariiraa o sulfonamides, "aminopyrine," "butadiene" me ētahi atu taero.

Hoki rōpū taua pānga āhuatanga e te aroaro i roto i te toto me te wheua wheua maha piringa o ngā wāhanga pūtau ki te matua ōrite, me puru nucleoli kotahi, kikokore, kahore he he cytoplasm potakataka.

Hāunga i erythrocytes hau angamaheni i roto i enei whatunga i motuhake muka pūpūira ngohengohe me whanganga. E kitea blastosis kōhikohiko ngaro kahore hahau me ngā awenga leukemoid hāngai ana i roto i nga tamariki whanau hou ki disorders pūira ira (hei tauira, Down syndrome).

momo tauhohenga Leukemoid e kua aroaro i runga, e kua hanga e runga i te papamuri o tetahi māuiuitanga, te tikanga e kore e meinga pōauautanga mōrearea. kia hetia kia i titiro te tahi taime tino puta thrombocytopenia rite tetahi o nga tohu o te kanisā whakapeka. Ko te rapunga immunoblastic lymphadenites nui faufaa ko te haumaru o te hanganga tūturu o te kōpuku waitinana, me te ki te whakatau tika i te raina o te follicles.

tauhohe Leukemoid me kanisā: ngā rerekētanga

He etahi rerekētanga i waenganui i taua pānga, me te kanisā, ara:

  1. A, no te tuimotu tauhohe faaapîraa i leukemoid wheua wheua tere, he reira metamielotsitarnym ka kitea hua i roto i ngā puka kanisā hau. A, no te ora pānga leukemoid erythroid iroriki, i reira te mea he ōwehenga leykoeritroblasticheskoe noa - 3: 1 me 4: 1.
  2. Ehara i faaiteraa kitea o te anaplasia ki ari leukemoid rite tupu te reira i roto i te kanisā, ka reira te mea he ngawha o te protoplasm me Pākatokato karihi.
  3. I roto i te whakatinanatanga tuatahi, i roto i te toto piringa kua he hua i roto i te maha tino me te ōrau o te hua i roto i neutrophils pakeke i roto i te te ihirangi kanisā heke neutrophils pakeke puta tini nui o taitamariki, puka teeki.
  4. A, no te tauhohe leukemoid pinepine kitea granularity paitini o neutrophils.
  5. A, no te leukocytes ako cytochemical i roto i te kanisā te hekenga ngaro ranei o te phosphatase kawakore, i tauhohe leukemoid - nui ake mahi.
  6. I roto i exacerbation o ma'i tapoko kanisā hau raruraru myeloid he eosinophilic, feohi basophilic ki tauhohe leukemoid reira tuimotu.
  7. A, no te maha e te thrombocytosis tiketike, me tauhohe leukemoid mōtepe kanisā myeloid tatau i roto i te whānuitanga noa.
  8. I roto i te wāhanga tuatahi o te kanisā myeloid ma'i kitea he kōateate nui mātotoru i tauhohe leukemoid ētahi wā tupu splenomegaly, engari he ngohengohe te tinana, me te kore tae te rahi rawa nui.
  9. A, no te tauhohe leukemoid ki te tukanga neoplastic kitea i roto i te pūtau mate pukupuku wheua wheua.

tauhohe Leukemoid i roto i ngā tamariki: hātepe tātaritanga

homai wāhi nui i roto i te tātaritanga o te mate te histopathology e tūhura rauemi unuhanga. Otiia i roto i te tikanga ki te karo hapa tūnguru, me kohikohi i te kairangahau mate pārongo tika e pā ana ki te manawanui, hoatu ki a ia te ahunga o te whakamātautau ngā me ki whakarite te maimoatanga cytostatic, e tango i nga hopearaa katoa o lymphadenitis. Ki te kore te tenei katoa meatia, i hanga te tātaritanga te tika, a na reira ki te akakoromaki i te mate, ka tino uaua kia. I muri i te katoa, ko te tino kino tenei mate. I te tahi taime, no te te mutunga o nga kōrero e tika ana ki te hanga unuhanga tukurua.

faufaa nui i roto i te Tātaritia i te ahua pani o waitinana biopsies kōpuku me te hāraunga. A, no te nuinga o te lymphosarcoma ngeniwhero (itinga 30 ōrau) fuoloa pūtau hau tamau. Ki te taua erythrocytes lymphadenitis immunoblastic, te tikanga iti iho i te 10 ōrau, e rerekē i roto i ngā o basophilia o cytoplasm me paari karihi ratou.

Me kia tino whai kiko, me te hāunga mutunga hē tātaritanga Histopathological i runga i te tātaritanga o te waitinana kōpuku. No te mea kia tautuhi histopathology o ngā rangahau o toto mārama te tātaritanga, me kitea tenei i roto i te mutunga. Hei tauira, mo te tātaritanga tuatahi o lymphoma Koló, i roto i ētahi wā, he wa roa ki te mau i te manawanui, me te ano titiro taikiri.

Tātaritanga tauhohe leukemoid whakapae ka kimi immunoglobulin monoclonal ētahi wā ko tā toutou me ngā kitenga wā roa- o wheua wheua poka. I mua ki te whakaaetanga o te tātaritanga o te hahau mate pukupuku contraindicated te.

kihi mate

Ko tētahi atu mate i huaina Filatov - Pfeyferra, glandular kirika, me te angina monocytic. Ko te mate viral āhuatanga e lymphocyte hau panoni, taikiri rahi me te kōateate, lymphadenitis urupare, te takanga o ngā pūtau toto whero motuhake i roto i te toto piringa. whakaaro te kaihoko pūtake te ki Epstein-Barr huaketo. Ko te pūtake o te mate - panoni hau o lymphocytes meinga e mate viral motuhake.

He rerekē te āhuatanga haumanu. I roto i te puka mähaki o Rhinitis tika ki te pakaru. āhuatanga Faaiteiteraa:

  • angina ( "tahu korokoro");
  • whakarahi o te kōateate me tīpona kōpuku me te mamae;
  • nasal kupukupu uaua i roto i nga ra wawe o te mate e tika ana ki te ngawhatanga o te mucosa.

Tūnga o te toto: hua i roto i te ōrau o eosinophils, lymphocytes me monocytes.

pōauautanga

E tika ana, me te rawaka mo te mutunga o te tohu o te mate, ko te aroaro i roto i te taketake toto mononuclear (i runga i te 10-20%) - pūtau e rerekē lymphocyte karihi cytoplasm nui, me te whanui basophilic ki te tae lilac ki te fakamaama perinuclear korerotia. Last tauhohe leukemoid i roto i ngā tamariki, me ngā pakeke mō te rave rahi wiki, engari marama tonu i roto i etahi āhuatanga, te māori o te huru toto.

Na kua kitea relapses ki te ngawari, i ētahi wā i wā o te maha nga tau i muri i te wā whakapeka tuatahi. kia ngā pōauautanga:

  • kakā whakapeka;
  • encephalitis;
  • agranulocytosis;
  • whaturama splenic meinga e tona hua tere;
  • hemolysis autoimmune.

Therapy tauhohe leukemoid

Ka rite ki te ture, e kore e tūroro rapua e rongoā motuhake, no te mea hoki he torutoru ra ngaro te tohu matua o te mate, me te āhua o te toto ki noa. A, no te roa mate me te manawanui ite māuiui whakamahia therapy pathogenetic - tautapa "prednisolone" i te horopeta o 20-30 mg te ra ranei te tahi atu raau taero glucocorticoid i roto i te tikanga ki te whakakore tauhohenga leukemoid. Treatment i roto i tetahi take, anake e whakaturia ana he tohunga.

outlook

Ko te tikanga pai: e kore he nui contagiousness, na e kore e te te manawanui e hiahiatia taratahi. Heoi, tino kino whaturama o te kōateate. Te whakatika whakaiti rōrahi whakaritea e nga āhuatanga ahua o te tinana, me te ngaro o te angina me māori o te pāmahana tinana. Ki te whakakitea mononucleosis hopuhopu te i roto i te puka o te kakā, e hiahiatia ana hohipera te manawanui.

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