Budd-Chiari syndrome

puta Budd-Chiari syndrome tika ki te obliteration whakamua (kati whāiti ranei) te lumen o te rua ringihia ki te ate. Chiari whakapono e te take matua - te mumura tuatahi o nga uaua ate. Otiia i muri mai i tāutuhia ai i roto i ētahi wā, i te Thrombosis o uaua ate me te iahoki vena cava iho.

whakaahua ana i te tuhinga āhua 200 take o te obliterating endoflebita i ate uaua (mate , Budd-Chiari syndrome).

Ki te whanaketanga o te thrombophlebitis arantsieva tau mahani, e wana tika ki te rua ate maui, rua pito, me tenei syndrome kia whakawhanake i roto i te kōhungahunga. Ko te anga o roto o nga uaua ate ranei vena cava iho Vienna (tata te pūruatanga o te ate) Kei te tipu, i ētahi wā piri e te clots toto. tenei katoa ai te kati whāiti ranei o te lumen o te rua, e, i roto i te tahuri, ai te whanaketanga o te stagnation me kōpeketanga o ngā pūtau ate.

whakawhanake hoki Budd-Chiari syndrome i roto i te tahi atu pathologies: neoplasms mārere o te ate, repe taiaki, whatukuhu, me ētahi atu, mate iaia āhua whakatakiruatanga. Ka taea hoki e Cirrhosis whai wāhi ki te whāiti o te uaua ate. Chiari syndrome kia meinga i te tetahi localization Gunma echinococcosis, actinomycosis, abscesses me pera i runga i.

Hauora, faaite Budd-Chiari syndrome tohu o te mate matua, meinga ana e ia he ti'aturi i runga i te roanga o te occlusion o uaua ano te atu whakaaturanga. tu te reira i roto i koi, me te putanga āta o te syndrome.

Whakapeka occlusion rua ate ai ahua ohorere o ruaki, te mamae i roto i te hautahi o runga tika epigastrium ranei e tika ana ki te ngawhatanga o te ate, me te hyperextension Glisson capsule, whanake ascites, i reira te mea he yellowness iti.

takawhita portal whanake i te wa ano hoki o te hua tere i roto i te pēhanga i roto i te sinusoids ate me uaua.

e kore te mea treatable ki Diuretics ascites ki tenei mate, hanga inu ake rawa hohoro ano i muri paracentesis, i ētahi wā whakanuia kia whakawhanake hydrothorax whiwhi ki ona toto,. Ki te hono Thrombosis e whakawhanake i roto i te iahoki vena cava iho, ka reira te huamo i roto i nga topito o raro, "upoko Medusa", me ki tono he pēhanga marama te ki reira, te toto haere ake.

Ki te hono te whanaketanga o ate katoa rua occlusion Thrombosis mesenteric, i reira he mamae, me te korere, puta tika ana ki te whara ate pūtau e arahi ki te mate i roto i te torutoru ra pōauautanga neurological.

I te tahi taime te syndrome Budd - kia Chiari, me te katinga wāhanga o te lumen o te rua puta rite te mate ma'i mo te wa roa. Ki te taua āhua o te rere o te wā puta tohanga hei utu: wewiti rua kiri fakangalingali, puta takawhita portal, a ka honoa me esophageal uaua tīponapona.

Hoki tātaritanga Ko aroaro faufaa o te pēhanga iti i roto i te uaua occlusal ate me te hua tukutahi o te pēhanga tomokanga, kitea nei e te tikanga o ngā tikanga hepato- me splenomanometrii. Whakamahia rentgenogepatografiya retrograde i roto i nei e whakaurua āpiha rerekē ki te rua ate. hāngai tātaritanga ultrasound te i runga i nga tohu tika - Imaging he katinga toto i roto i te uaua.

Te kore tae rangahau doplerrovskogo whakaaro Budd-Chiari syndrome i roto i:

• Ko te aroaro o huringa E ruia ana i roto i te ate, āhuatanga o nui ate fatty ranei kakakīrehe o te kiko ate,

• Ko te pikitia kahore uaua ate, puranga hei tauira, e tika ana ki te aroaro i roto i to ratou lumen fakaongo-pai i roto i te lumen,

• he whāiti o te iahoki vena cava iho,

• tohu o takawhita tomokanga, ki te roa te mate te.