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Granulomatosis o Wegener - Take, tohu, maimoatanga.

granulomatosis o Wegener - ko te mate autoimmune āhuatanga e mumura o nga pera iti me uaua. I roto i te nuinga o te wā i te iatuku matia tuku toto sinuses, pūkahukahu me te tākihi te kopa, engari, i roto i te tua, i reira he āhua wāhanga i roto i te kaupapa e pā anake tetahi o enei rohe. Ki te granulomatosis whānui miharo tata tonu i te pūkahukahu e rua me nga whatukuhu e rua. I roto i taua take, ki te te pāngia e te marama anake nga whatukuhu anake ranei, ko reira he mate i huaina granulomatosis o Wegener pahara.

Ko te nuinga noa i roto i te iwi teina waenganui-koroheke ranei granulomatosis o Wegener, tata kahore te whakatutuki i te tamariki. Ko, ahakoa, te mate taea ki te pā ngā rōpū pakeke katoa ko te. tatauranga Ira hinga rerekē tenei mate i roto i rerekē kaituhi.

Ko te take o te mate

Ko te take o taua mate, pērā i granulomatosis o Wegener, e kore e matau tino tenei ra. He maha ngā tohunga whakapono e kia te take o te mate, he kaihoko viral, no te mea maha puta granulomatosis o Wegener i muri werohanga, mahaha, therapy paturopi te rongo ranei. Ko, kāore, kua tonu e kore tohaina te kaihoko koiora, na whakaaro te mate te he autoimmune.

Ētahi tūroro whakapoauau poradenitis me granulomatosis o Wegener. kia mohio ki te reira e te ōrite o te tohu e rua mate tino rerekē no te mea whakatika poradenitis tika ki tukumate kitakita (Chlamydia), i te granulomatosis o Wegener ko te mate autoimmune.

Tohumate me te puka mate

Ka taea e granulomatosis o Wegener timata ohorere, engari kia mura ake āta. Ko te tohu tuatahi taea te whakaaro o te mate subfebrile pāmahana, ka heke te reira hiahia. I muri nei te pāmahana tīmata ki te whakatika, me te ahunga whakamua mate.

Ko te tohu noa o tenei mate ngā:

- mate taimaha;

- rohirohi;

- te whakatairanga i te pāmahana;

- te mamae i roto i te hononga;

- te mamae i roto i te mumura pakohu.

I tua atu, ka taea e te mate pā wāhanga ngā o te tinana, hoatu he tohu tino rerekē. Hei tauira, ki te hinga o te ihu e mātihetihe romahā waho ki purulent wehenga kino toto, necrotic mucosa nasal, me te te mangai ngohengohe me tonsils.

He puka te whakatakiruatanga o o te mate e homai he marama torutoru, he pōauautanga nui o te kiri, i roto i ngā, kitea toto, nodular, āhuatanga necrotic, a i roto i te tahi mau rōpū o tūroro, me pericarditis, myocarditis Bronchitis ranei.

tātaritanga o te mate

Matua hoki whakapae me tūroro granulomatosis o Wegener haere urinalysis mo te aroaro o te pūmua, me te toto whero ngā pūtau i roto i te mimi. E hanga atu whakapakoko X-ray sinuses me pouaka, kia kite i te huringa pathological. Ano, tangohia tātaritanga o toto te ka, i roto i ngā, i whakaritea e te ESR me te pūmua C-urupare. He he ano hoki te tātaritanga atu matatini, engari ano hoki atu whai hua ki te tāutu i ngā paturopi cytoplasmic antineyrofilnyh.

maimoatanga o te mate

granulomatosis o Wegener, kahore maimoatanga tika kia pai arahi i te manawanui ki te mate e rua ki te toru marama i roto. Kei te nuinga hāngai maimoatanga katoa i te pehanga o te pūnaha ārai mate, me te tauhohe inflammatory rohe. Ko te taero tino rongonui he corticosteroids me cyclophosphamide. kia ēnei raau taero kia tangohia ra ano murunga o te mate, a ka ki kahore Maoritanga mate o Hodgkin, e taea te tāpiri ki a ratou ano, ka methotrexate, e kia tango o tau i te tokorua.

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