Syndrome Lennox-Gastaut (haurangi)

Lennox-Gastaut syndrome - he puka o te haurangi (myoclonic-astatic). mate taua ahua tā te huinga o te toniki me haurangi atonic, haurangi ngaro mohiotia, whakaroa whanaketanga hinengaro i roto i nga kohungahunga. Ka taea e hoki te wa tuatahi te mate faaite mai ano i roto i ngā tamariki i tetahi ki te e rima, nuinga hoki tamariki.

te nuinga o whanake tēnei mate rite ki te hua whakawhiti ki te kōhungahunga mate neurological, a ka haamata ki te maturuturunga iho ohorere i roto i te tamaiti. I muri i te tahi wa, i reira he haehae, hukihuki, faaite whanaketanga hinengaro puhoi, me maramarama iti.

Ina e, ki te tupu o te tamaiti, te āhua o hukihuki rerekē. Hinga whakakapia e te kanohi, tuarua ko nga te whakatakiruatanga o, patua matatini o te haurangi.

No te mea o te mea e whakaaturia ana te syndrome Lennox-Gastaut

Hei mahino nga take o tenei syndrome ko nui uaua, engari ki te rā mohiotia ko nga mea matua.

• Ko te Pākatokato o te whanaketanga roro.
• mate kino (meningitis, encephalitis, kōpukupuku).
• Ira mate roro pathological (CNS, mate pūkoro tinana, sclerosis tuberculous).
• tamaiti whara i roto i te wahi o te awa whanautanga (whanautanga asphyxia, whanau taimi halá, me ētahi atu).
• whara CNS i roto i te wā perinatal, me te tuku preterm me asphyxia.

tohu o PLGA

Ka taea te mohio Lennox-Gastaut syndrome i te tohu tino nui - no te hukihuki. Tamariki nei e pāngia ki "haurangi idiopathic", e pā ana hoki ki ngā ngā o te haurangi (tohu) :

• paroxysms o taka;
• hukihuki atonic;
• ma'iriraa mohiotia;
• hukihuki wāhanga;
• cramps sternocleidomastoid;
• haurangi myoclonic-astatic;
• haurangi toniki (te tikanga puta i roto i te moe au tonu);
• TC te whakatakiruatanga o hukihuki.

Tūroro ki te syndrome o Lennox-Gastaut i hoki te āhua āhuatanga o te hiamoe ki te whakawhitinga maeneene i roto i haurangi, te retardation hinengaro, hinengaro, me te disorders tuakiri.

Tātarihia te te syndrome LH

i muri tonu kia rapu tonu nga tohu tuatahi o te mate tokoni ngaio, karanga te waka tūroro. Tikanga, kawea tātaritanga o te mate i roto i te whakamahi i ECG i waenganui whakaeke.

LH Syndrome Treatment

tukinotia Lennox-Gastaut syndrome te ki rongoā me tikanga hāparapara. Treatment ki ngā rongoā ki te tukua hua pai i roto i kore ake atu i te 20% o te wā. I roto i te tikanga maimoatanga hāparapara mō te whakakore pata ohorere, he reira whai hua ki te tapahia te io hono (callosotomy). Ano, whakahaua whakamahi mahi ki te whakaongaonga o te karere vagus me tango o pukupuku iaia me malformations.

Heoi, kia tuhia te reira e te mea maha uaua ki te hamani haurangi āhuatanga o tenei syndrome; i roto i te mutunga kia meinga ratou te manawanui ki kino hopearaa pāpori, me te hinengaro. haurangi toniki Tata untreatable, e arahi ki te raro maramarama.